Myoclonic absence seizures with complex gestural automatisms.
| Author | |
|---|---|
| Abstract | :
Epilepsy with myoclonic absences is a rare generalized epilepsy syndrome with distinctive seizures. Two unrelated children had mild developmental impairment and onset of myoclonic-absences at 3 and 8 years. Seizures were characterized by bilateral 3 Hz myoclonic jerks superimposed on tonic abduction of the upper limbs. Events lasted 10-60 s, and complex gestural automatisms were often observed; in one case, a boy undid his seatbelt and attempted to exit a moving vehicle. Post-ictally, both children immediately regained awareness without recollection of their actions. Ictal EEGs showed 3 Hz generalized spike-wave. Complex automatisms have not been described in myoclonic absence seizures. This generalized seizure type can be confused with focal seizures when these ictal behaviours occur. |
| Year of Publication | :
2017
|
| Journal | :
European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society
|
| Date Published | :
2017
|
| ISSN Number | :
1090-3798
|
| DOI | :
10.1016/j.ejpn.2017.12.003
|
| Short Title | :
Eur J Paediatr Neurol
|
| Download citation |